《英文msh詞典》Muscular Dystrophy,Becker
[同義詞] Muscular Dystrophy,Becker
[主題詞] Muscular Dystrophy,Duchenne
[中文釋義] 肌營養(yǎng)不良,貝克爾
[英文釋義] An X-linked recessive muscle disease caused by an inability to synthesize DYSTROPHIN,which is involved with maintaining the integrity of the sarcolemma. Muscle fibers undergo a process that features degeneration and regeneration. Clinical manifestations include proximal weakness in the first few years of life,pseudohypertrophy,cardiomyopathy (see MYOCARDIAL DISEASES),and an increased incidence of impaired mentation. Becker muscular dystrophy is a closely related condition featuring a later onset of disease (usually adolescence) and a slowly progressive course. (Adams et al.,Principles of Neurology,6th ed,p1415)